Retina/Uveitis Quiz 19
Rosa Y. Kim, MD | Massachusetts Eye and Ear Infirmary, Harvard Medical School
May 27, 1997
Figure 1
Figures 1-3. This is a patient who had 20/20 vision OU and was found to have these fundus and fluorescein findings.
Figures 1-3. This is a patient who had 20/20 vision OU and was found to have these fundus and fluorescein findings.
Figure 2
Figure 3
Answer: Sjogren's reticular dystrophy of RPE, characterized by an accumulation of dark pigment in a meshwork or fishnet-like pattern. This is an extremely rare condition.
2. What is the inheritance pattern of this condition?
Answer: Autosomal recessive
3. Does the pigmentary pattern in this condition change over time?
Answer: The network of pigment starts centrally, then extends toward the periphery in later stages of the disease, and finally disappears.
4. How is the vision affected?
Answer: Vision is usually unaffected in this condition
5. What would an ERG SHOW in this condition?
Answer: Both full field and foveal ERGs are normal.